Anaesthetic management of an infant with Epidermolysis Bullosa undergoing inguinal hernia repair

Epidermolysis bullosa is a group of inherited disorders characterized by blistering of the skin as a result of minor trauma. We managed an infant with epidermolysis bullosa undergoing inguinal hernia repair. Anaesthesia was induced with oxygen/nitrous oxide mixture and sevoflurane. Oral tracheal intubation was done with a lubricated laryngoscope blade with KY jelly using atracurium 0.5mg/kg and fentanyl 0.1μgm/kg. To avoid frictions on the skin, endotracheal tube was tied with ribbon gauze and fixed around the neck. Pulseoximetry probe and electrocardiogram electrodes were placed, and then attached to the patient s skin covered with KY jelly. Peripheral venous access was secured in the right foot and sutured. These methods were effective to avoid new blisters and useful for infant safety.