Author/Authors :
Sparks, Dorothy Northeast Ohio Medical University - College of Medicine - Western Reserve Care System, USA , Chase, Daniel Northeast Ohio Medical University - College of Medicine - Western Reserve Care System, USA , Thomas, David Northeast Ohio Medical University - College of Medicine - Western Reserve Care System, USA , Arnott, Jon Northeast Ohio Medical University - College of Medicine - Western Reserve Care System, USA
Abstract :
The Wunderlich Syndrome refers to spontaneous perirenal hemorrhage often associated with underlying renal pathology. We report the case of a 23-year-old female with advanced tuberous sclerosis who presented in hypovolemic shock secondary to rupture of one of her massive bilateral angiomyolipomas (AMLs). The patient was able to be managed conservatively and subsequently retained full renal function. A review of the literature with a discussion of types of clinical presentation,diagnostic criteria,and methods of management of AMLs is included.
