Author/Authors :
Saygıli, Özlem Barutçu Acıbadem Bakırköy Hospital - Department of Radiology, Turkey , Saygılı, Arda Acıbadem Bakırköy Hospital - Department of Pediatric Cardiology, Turkey , Erek, Ersin Acıbadem Bakırköy Hospital - Department of Cardiac Surgery, Turkey , Sarıoğlu, Ayşe Acýbadem Bakýrköy Hospital - Department of Pediatric Cardiology, Turkey , Sarıoğlu, Tayyar Acıbadem Bakırköy Hospital - Department of Cardiac Surgery, Turkey
Abstract :
Interrupted aortic arch with intact ventricular septum is a rare severe congenital heart defect defined as a complete loss of luminal and anatomic continuity between ascending and descending aorta without ventricular septal defect. A 8-year-child referred to our center for cardiac operation from Irak. Preoperative echocardiographic evaluation showed enlarged left ventricular dimension is and severely diminished systolic function. Aortic valve was found to be bicuspid with mild gradient. Aortic arcus was interrupted below the left subclavian artery. Large patent ductus arteriosus was established to be supplying the descending thoracic aorta. The patient underwent the heart catheterization for the hemodynamic study.
