Author/Authors :
Özdemir, Sonay İncesoy Dr. Sami Ulus Children s Hospital - Clinic of Pediatric Oncology, Turkey , Bozkurt, Ceyhun Dr. Sami Ulus Children’s Hospital - Department of Pediatric Oncology, Turkey , Örün, Arman Dr. Sami Ulus Children s Hospital - Clinic of Pediatric Cardiology, Turkey , Şahin, Gürses Dr. Sami Ulus Children’s Hospital - Department of Pediatric Oncology, Turkey , Yüksek, Nazmiye Dr. Sami Ulus Children’s Hospital - Department of Pediatric Oncology, Turkey , Çetinkaya, Semra Dr. Sami Ulus Children s Hospital - Clinic of Pediatric Endocrinology, Turkey , Ertem, Ulya Dr. Sami Ulus Children’s Hospital - Department of Pediatric Oncology, Turkey
Abstract :
Pulmonary arteriovenous malformation (PAVM) is a rare cause of cyanosis in early infancy. PAVMs are direct communications between the smaller pulmonary arteries and veins (1, 2). Pulmonary arteriove- nous malformation in its acquired form usually occurs in juvenile cirrhosis, but has also been reported in patients with trauma, pulmonary schistosomiasis, mitral stenosis, actinomycosis, Fanconi syndrome, and metastatic thyroid carcinoma (3). However, as far as we know infantile hepatic hemangioendothelioma (IHHE) which consists of clinical triad including hepatomegaly, congestive heart failure, and cutaneous hemangiomas with coexistent PAVM has not been reported. Here, we describe this unusual presentation.
