Author/Authors :
Özbudak, Ersan Kocaeli University - Faculty of Medicine - Department of Cardiovascular Surgery, Turkey , Arıkan, Ali Ahmet Kocaeli University - Faculty of Medicine - Department of Cardiovascular Surgery, Turkey , Yavuz, Şadan Kocaeli University - Faculty of Medicine - Department of Cardiovascular Surgery, Turkey , Halıcı, Ümit Samsun Education and Research Hospital - Clinic of Cardiovascular Surgery, Turkey , Berki, Turan Kocaeli University - Faculty of Medicine - Department of Cardiovascular Surgery, Turkey
Abstract :
Sinus histiocytosis (Rosai-Dorfman Disease) is a rare disease, which is characterized by massive lympadenopathies with unknown etiology. It was first defined in 1969 by Rosai and Dorfman (1). Although it is seen most frequently in the first two decades of life, it can be observed at any age. The frequency of cardiac involvement is less than 1% in Rosai-Dorfman disease (RDD) (2). Here, we report a case with extranodal RDD in which cardiac involvement was detected.