• Title of article

    Case of fatal heart failure with biventricular noncompaction, genital skeletal abnormalities and mental retardation

  • Author/Authors

    Ataş, Halil Marmara University Trainingand Research Hospital - Department of Cardiology, Turkey , Samadov, Fuad Educational-Therapeutic Clinic of Azerbaijan University - Department of Cardiology, Azerbaijan , Sarı, İbrahim Marmara University Trainingand Research Hospital - Department of Cardiology, Turkey , Delil, Kenan Marmara University Trainingand Research Hospital - Department of Genetic, Turkey

  • From page
    71
  • To page
    72
  • Abstract
    Noncompaction cardiomyopathy (NC) is rare a genetic disorder. Although it is generally associated with additional cardiac and extracardiac disorders (1), cases with genital anomalies are extremely rare. Here we report a 48-year-old female with biventricular noncompaction, mental retardation, ovarian dysgenesis, uterine aplasia, bilateral amazia, and skeletal anomalies.
  • Journal title
    The Anatolian Journal of Cardiology: Andolu Kardiyoloji Dergisi
  • Journal title
    The Anatolian Journal of Cardiology: Andolu Kardiyoloji Dergisi
  • Record number

    2693131