Anhidrotic Ectodermal Dysplasia with Palmoplantar Keratoderma: A Rare Presentation

Anhidrotic ectodermal dysplasia (AED) is characterized by a partial or complete absence of sweat glands, hypotrichosis and hypodontia. Palmoplantar keratoderma is classically a component of hidrotic ectodermal dysplasia; 1 however, I report here in two brothers who had classical manifestations of AED along with palmoplantar keratoderm.