Author/Authors :
Akbarzadeh Pasha, Abazar Cancer Research Center - Health Research Institute - Babol University of Medical Sciences, Babol , Shafi, Hamid Clinical Research Development Center - Shahid Beheshti Hospital - Babol University of Medical Sciences, Babol , Teimorian, Mohammad Department of Urology - Shahid Beheshti Hospital - Babol University of Medical Sciences, Babol , Rostami, Ghasem Babol University of Medical Sciences, Babol , Nasirimehr, Khatereh Babol University of Medical Sciences, Babol , Moudi, Emadoddin Cancer Research Center - Health Research Institute - Babol University of Medical Sciences, Babol
Abstract :
Background: Congenital adrenal hyperplasia (CAH) refers to group of congenital diseases
resulting from impaired adrenal steroidogenesis, and its most common cause is 21-
hydroxylase deficiency. Testicular adrenal residual tumor (TART) is one of the major
complications of CAH, possibly resulting from ectopic remnants of intra-testicular adrenal
tissue which is stimulated by excessive secretion of adrenocorticotropic hormone (ACTH).
This tumor can be misdiagnosed as Leydig cell tumor (LCT) in these people.
Case Presentation: The patient we are presenting is a 20-year-old man with a history of
precocious puberty and a height below 3% of the population who underwent radical left
testicular orchiectomy with a complaint of bilateral testicular mass, which is reported LCT
in the pathology report. In preoperative imaging examinations, bilateral adrenal hyperplasia
is observed. In hormonal examinations, the patient is diagnosed with CAH and has been
treated with corticosteroids for one year.
Conclusion: In patients who present with bilateral testicular mass, it is the best image by
abdominopelvic CT scan before surgery to detect CAH.
