Author/Authors :
nijhawan, manisha mahatma gandhi medical college and hospital - department of skin, venereology and leprosy, Jaipur, India , agarwal, savita mahatma gandhi medical college and hospital - department of skin, venereology and leprosy, Jaipur, India , nijhawan, shivi mahatma gandhi medical college and hospital - department of skin, venereology and leprosy, Jaipur, India , jhangra, rakesh mahatma gandhi medical college and hospital - department of skin, venereology and leprosy, Jaipur, India , goel, pallavi mahatma gandhi medical college and hospital - department of skin, venereology and leprosy, Jaipur, India , sehgal, virendra n. dermato venereology (skin/vd) center - sehgal nursing home, Delhi, India
Abstract :
Epidermolysis bullosa pruriginosa, a rare variant of dominant inheritance pattern, characterized by itchy, papules and/or nodules coalescing to form plaque(s), studded by blisters, is describe in a young man an index case. In all 12 afflicted individuals of the 27 family members was interesting, the diagnosis of which was made by its morphology and inflammatory changes in the epidermis, comprising hyperkeratosis, moderate acanthosis, presence of inflammatory cells, and above all inflammatory cell containing sub-epidermal cleavage or cleft.
Keywords :
Epidermolysis bullosa , Hallopeau , Siemens , Dystrophic epidermolysis bullosa