Author/Authors :
torino, giovanni santobono-pausilipon children s hospital - pediatric urology unit, Naples, Italy , adorisio, ottavio bambino gesù children’s hospital - research institute - department of pediatric surgery, pediatric surgery unit, Rome, Italy , cobellis, giovanni marche polytechnic university - “g. salesi” children’s hospital - pediatric surgery and urology unit, Ancona, Italy , mariscoli, francesca marche polytechnic university - “g. salesi” children’s hospital - pediatric surgery and urology unit, Ancona, Italy , zaccara, antonio bambino gesù children’s hospital - research institute - department of pediatric surgery, pediatric surgery unit, Rome, Italy
Abstract :
The Disorders of Sex Differentiation (DSD) represent a wide range of congenital anomalies of the genitalia. Surgical treatment of these cases may become a challenge. We present a case of a 16-year-old boy with 46 XX DSD, SRY negative, presented with persistent dribbling incontinence, recurrent UTI, and perineal pain. Past medical history included right orchiectomy, laparoscopic excision of uterus, fallopian tubes, and left streak gonad at another institution at the age of 2 years. The native vagina was left in place. VCUG confirmed the presence of the residual vagina (8 cm in maximum length), connected with the bulbar urethra. Robotic-assisted laparoscopic excision of the vagina was performed with satisfying short and long-term results
Keywords :
robotic surgery , DSD , UTI , pelvic surgery , minimally invasive surgery
