Carneyʹs Triad

The purpose of this study is to provide an overview of cases of Carneyʹs triad and to discuss the clinical implications of this diagnosis. A search was made of the English-language literature for original articles, reviews and abstracts addressing Carneyʹs triad. A new patient was described and added to the number of known patients. In literature 40 patients were found with a complete or incomplete triad. There exists no agreement on the pathology and possible common origin of these tumours. Directions are given for diagnostics and therapy. The diagnosis of Carneyʹs triad has specific clinical implications that make a good knowledge of this syndrome mandatory.