Repair of double-chambered right ventricle: surgical results and long-term follow-up

Background. We reviewed the outcomes of double-chambered right ventricle repair. Methods. Between 1969 and 1998, 40 patients underwent surgical repair of a double-chamber right ventricle. The patients ranged in age from 3 months to 52 years (mean, 12.8 ± 11.6 years). Right ventricular outflow tract pressure gradients were from 20 to 170 mm Hg (mean, 65.0 ± 38.5 mm Hg) An associated ventricular septal defect was present in 27 patients (67.5%). Four patients were older than 30 years of age. Results. There were no hospital or late deaths. Mean postsurgical follow-up was 16.5 ± 8.9 years (range, 2.5 to 31 years). No patient required further surgery to relieve obstruction of right ventricular outflow tract. Conclusions. Surgical repair of a double-chambered right ventricle yields excellent hemodynamic and functional results over both the short and long term.