Author/Authors :
Eduardo Bernabeu، نويسنده , , Miguel Josa، نويسنده , , Benet Nomdedeu، نويسنده , , José Ramirez، نويسنده , , Antonio Garc?a-Valent?n، نويسنده , , Carlos A. Mestres، نويسنده , , Jaime Mulet، نويسنده ,
Abstract :
Wiskott-Aldrich syndrome is a primary immunodeficiency characterized by infections, thrombocytopenia, and eczema. We present a 33-year-old man with this syndrome who underwent a one-stage ascending aorta, aortic arch and descending aortic aneurysm repair under moderate hypothermia and continuous visceral and cerebral perfusion. Histologic examination showed the presence of an aortitis with granulomatous inflammatory response and multinucleated cells.
