Primary Hypertrophic Cardiomyopathy in Noonan Syndrome

We describe a case of Noonan syndrome referred to the department of pediatric cardiology for routine evaluation of cardiovascular abnormalities. Physical examination, electrocardiogram, chest X-ray and echocardiographic finding confirmed severe hypertrophic cardiomyopathy in the absence of any other cardiac abnormalities or systemic condition (Iranian Heart Journal 2007; 8 (1): 52- 54).