Author/Authors :
Hashemi، A نويسنده Department of Pediatrics, Hematology, Oncology and Genetic Research Center, Shahid Sadoughi University of Medical Sciences Health Services, Yazd, Iran , , Tefagh، S نويسنده MD, Hematology, Oncology and Genetics Research Center, Shahid Sadoughi University of Medical Sciences and Health Services, Yazd, Iran. , , Seifadini ، A نويسنده Department of Medical Sciences, Yazd Branch, Islamic Azad University, Yazd, Iran. , , Moghimi ، M نويسنده Department of Pathology, Shahid Sadoughi University of Medical Sciences Health Services, Yazd, Iran. ,
Abstract :
Abstract
Background
Infantile Fibrosarcoma is a rare soft tissue tumor in infants and children mostly located in extremities. An infantile and adult form has similar histopathological patterns but survival prognosis is much better in infantile form. Recurrence of infantile fibrosarcoma is common but the rates of metastasis are less than 10 percent in children younger than five Years and 50 percent in children more than 10 years old.
Case presentation
In this case report, we presented a nine years girl with a relapsing mass in her left hand. The pathologic
findings showed sheets of spindle-shaped cells with suggested diagnose of infantile fibrosarcoma. She was successfully treated with combination of surgery and chemotherapy with a good outcome.
Conclusion
Infantile fibrosarcoma is a differential diagnose of soft tissue mass in infants and children. It has a good prognosis and distant metastasis is uncommon. Choice of treatment is surgery but chemotherapy and radiotherapy were useful in decrease metastasis.
