Author/Authors :
Türk, B G Ege Üniversitesi - Tıp Fakültesi - Dermatoloji Anabilim Dalı, Turkey , Ertekin, B Ege Üniversitesi - Tıp Fakültesi - Dermatoloji Anabilim Dalı, Turkey , Sezgin, A Ö Ege Üniversitesi - Tıp Fakültesi - Dermatoloji Anabilim Dalı, Turkey , Kazandı, A C Ege Üniversitesi - Tıp Fakültesi - Dermatoloji Anabilim Dalı, Turkey , Dereli, T Ege Üniversitesi - Tıp Fakültesi - Dermatoloji Anabilim Dalı, Turkey , Özdemir, F Ege Üniversitesi - Tıp Fakültesi - Dermatoloji Anabilim Dalı, Turkey
Abstract :
Scleromyxedema is a chronic, rare disease with an unknown etiology which is characterized by fibrosis and mucin deposition in dermis and monoclonal gammopathy. Scleromyxedema is differentiated from the other cutaneous mucinoses with the presence of mucin deposition with fibrosis, generalized papular and sclerodermoid eruption, monoclonal gammopathy and with the absence of a tiroid disorder. The other organ systems may also be involved. The treatment of the disease is particularly difficult. Because of the rarity of the disease, experience with the treatment is limited to case reports and series. Therefore herein, a dramatic resolution of scleromyxedema with systemic streoid treatment is presented.
