Author/Authors :
TAS, Adnan Osmaniye Public Hospital - Gastroenterology, Turkey , ARHAN, Mehmet Ankara Education and Research Hospital - Gastroenterology, Turkey , AKSOY, Sercan Ankara Numune Education and Research Hospital - Oncology, Turkey , KOKLU, Seyfettin Ankara Education and Research Hospital - Gastroenterology, Turkey
Abstract :
Desmoplastic small round cell tumour (DSRCT) is a malignant pathologic entity with a mesothelial origin. It is a rare neoplasm of small round cells located in the abdomen, mainly affecting male adolescents and young adults. Herein, we report a 17-year-old man presented with ascite and growing very fast abdominal mass. Laparoscopy was performed showing thickening of omentum and peritoneum and normal internal organs. Histopathologi-cal examination of the peritoneal samples concluded to desmoplastic small round cell tumor. The patient was treated according to the cyclophospha-mide, vincristine and adriamisin. He responded chemotherapy and reduced intraabdominal, pelvic ascites and intraabdominal masses.