Kahraman, Erkan Eskişehir Asker Hastanesi - Kulak Burun Boğaz Kliniği, Turkey , Öztürk, Cengiz Eskişehir Asker Hastanesi - Kardiyoloji Kliniği, Turkey

Kartagener Syndrome With Interatrial Septal Aneursym and Congenital Atrioventricular Block: Two Case Reports

20153

The Kartagener syndrome is a rare autosomal recessive disorder characterized by bronchiectasis, sinusitis, situs inversus. Primary ciliary dyskinesia is condition with a prevalance of 1 in 20000 live births and fifty percent of primary ciliary dyskinesia is Kartagener’s Syndrome. Kartegener syndrome; may be accompanied with cardiac abnormalities such as ventricular septal defect (VSD) and atrial septal defect (ASD) in addition to dextrocardia. In this article, as addition to above-mentioned abnormalities, existence of two different cardiac problems together at the same time is reviewed with clinical, radiological and echocardiographyic characteristics by means of taking the literature into consideration.

181

Kartagener syndrome , interatrial septal aneurysm , congenital atrioventricular block

Gulhane Medical Journal

183