Author/Authors :
Gökçe, Şule Ege Üniversitesi - Tıp Fakültesi - Çocuk Sağlığı ve Hastalıkları, Turkey , Koç, Feyza Ege Üniversitesi - Tıp Fakültesi - Çocuk Sağlığı ve Hastalıkları, Turkey , Turan, Gülizar Ege Üniversitesi - Tıp Fakültesi - Çocuk Sağlığı ve Hastalıkları, Turkey , Örsdemir, Hacer Ege Üniversitesi - Tıp Fakültesi - Çocuk Sağlığı ve Hastalıkları, Turkey , Dökümcü, Zafer Ege Üniversitesi - Tıp Fakültesi - Çccuk Cerrahisi, Turkey , Elekberova, Vüsale Ege Üniversitesi - Tıp Fakültesi - Çccuk Cerrahisi, Turkey , Akşit, Sadık Ege Üniversitesi - Tıp Fakültesi - Çocuk Sağlığı ve Hastalıkları, Turkey
Abstract :
Lymphedema is a disease that is caused by the blockage of flow of lymph and is generally characterized with swelling (edema) in the extremities. Primary lymphedema which is rarely seen can develop either at birth or symptoms can begin at puberty and is known as lymphedema praecox. Lymphedema praecox is the most common form of primer lymphedema and is diagnosed by the exclusion of secondary causes. Lymphatic Dysplasia Syndrome is defined as primary lymphedema with effusion in the third spaces of the body such as the pleura, pericardium and peritoneum. In this article, we present a rare case of a 14 year old girl who was diagnosed with lymphedema praecox/lymphatic dysplasia syndrome because she had edema in both her lower extremities and chylothorax in her right lung.
