Author/Authors :
Akpına, Funda Pamukkale Üniversitesi - Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları AD, Denizli , Özdemir, Emine Pamukkale Üniversitesi - Tıp Fakültesi, Çocuk Sağlığı ve Hastalıkları AD, Denizli , Balcı, Yasemin Işık Pamukkale Üniversitesi - Tıp Fakültesi, Çocuk Hematoloji ve Onkolojisi AD, Denizli , Polat, Aziz Pamukkale Üniversitesi - Tıp Fakültesi, Çocuk Hematoloji ve Onkolojisi AD, Denizli
Abstract :
Purpose:Despite prophlactic treatment and patient-family education, in hemophilia patients, the most common cause of emergency visits is known as trauma.Materials and methods:In this study, hemophilia patients that were administered to a university hospital emergency department were investigated in terms of their demographic information, administration causes based on infection, type of trauma, bleeding sites retrospectively.Results:While the mean age of hemophilia A patients were 16.6±9.1(1-32), mean age of hemophilia B patients were 17.1±7.1(5-27). One of the hemophilia A patients has moderate, another one mild type of hemophilia and others had severe type of hemophilia. For hemophilia B patients, two of them had moderate type, others had severe type hemophilia. Only one patient uses prophylactic factor replacement treatment. None of the patients has had inhibitor positivity. In between 2007-2013 years, 13 Hemophilia A patients visited emergency department 381 (70%) times and 7 hemopfilia B patients visited 166 (30%) times. Eighty seven percent of these visits belonged to severe type of hemophilia patients, 13% of them belonged to mild and moderate type hemophilia patients. The 311 (%57) of 547 visits were due to trauma or bleeding, 236 (43%) of them were factor treatment. Bleeding sites were, joint (n: 248), epistaxis (n:18), mouth (n:14), hematuria (n:14), iliopsoas muscle (n:5), head trauma without intracranial bleeding (head to head crashing, television and shelf dropping n:5),hematoma after insect bite (n:4), anal-scrotal hematoma after riding bicycle (n:3). Conclusion: As a result, in spite of excess of joint bleeding, it was pleasing that there were not any intracranial bleeding. On the other hand, the high amount of administrations due to factor replacement therapy suggested that self-infusion education was insufficient. Family and patient education for hemophilia patients to protect them from home accidents must be increased and must be continuous.
