Yıldız, Özlem Kayım Cumhuriyet University - School of Medicine - Department of Neurology, Turkey , Çevik, Şeyda Cumhuriyet University - School of Medicine - Department of Neurology, Turkey , Öztoprak, İbrahim Cumhuriyet University - School of Medicine - Department of Radiology, Turkey , Bolayır, Ertuğrul Cumhuriyet University - School of Medicine - Department of Neurology, Turkey , Topaktaş, Suat Cumhuriyet University - School of Medicine - Department of Neurology, Turkey

Foix-Chavany-Marie syndrome due to a unilateral opercular infarction

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Bilateral paralysis of facial, pharyngeal, lingual, and masticatory muscles with automaticvoluntary dissociation characterizes Foix-Chavany-Marie syndrome (FCMS). The syndrome is a rare neurological disorder which usually develops secondary to cerebrovascular accidents affecting bilateral opercular regions, typically as a result of subsequent strokes. A 75-year-old woman presented with acute onset of inability to speak and swallow. Neurological examination demonstrated bilateral palsy of lower motor cranial nerves with preservation of reflex and automatic movements. Magnetic resonance images of the brain showed an acute right frontal opercular infarction and old subcortical lacunar infarctions in the bilateral hemispheres. Although FCMS occurs due to bilateral opercular lesions, rarely unilateral opercular lesion accompanied by contralateral subcortical lesions may cause the typical clinical features of the syndrome.

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Opercular syndrome , Foix , Chavany , Marie syndrome, Pseudobulbar pals

Cumhuriyet Medical Journal

256