گزارش يك مورد رزكسيون جراحي موفقيت آميز فيستول شرياني - وريد ريه

Pulmonary Arteriovenous Malformation : A Case Report with Successful Surgical Results

Pulmonary Arteriovenous Fistula ( PAVF ) is one of the most rare congenital malformations of the pulmonary vasculature and most of them are seen in association with congenital hereditary hemorragic telangiectasia ( Rendu- Oster- Weber syndrome) . Although most of these patients are asymptomatic , they may be presented with signs and symptoms like dyspnea , cyanosis , hemoptysis, hemothorax and clubbing of fingers . Rarely it may be complicated with transient ischemic attacks (TIA ) or stroke and brain abscess . Angiography is the standard procedure for diagnosis of PAVF but spiral CT has also been used with comparable results . Because of complications of PAVF most of patients need some kinds of treatment . Surgery and pulmonary artery embolization are the two main treatments of choice in this condition . We present a 13 year- old boy with headache, hemoptysis and dyspnea who was admitted with hemoptysis and early fatiguability on exertion . Radiology examination showed lobulated mass in RLL and right hilum . Finally surgical intervention proved excellent results. Surgery is the best treatment of isolated ( single ) AVM or PAVF.