گزارش يك مورد اصلاح ناهنجاري دنتوفاسيال به روش جراحي در بيمار مبتلا به تالاسمي ماژور

Correction of dentofacial deformity in a thalassemic patient with orthognathic surgery: A case report

Introduction: Thalassemia is a genetically determined disorder of hemoglobin syntheses which results in problematic erythropoisis and finally leads to compensative dilation of bone marrow spaces and associated multiple skeletal disorders. These patients routinely are under hyper transfusion and in some cases spelenectomy may be accomplished. Treatment of dentofacial deformities in these patients is a complicated procedure because of possibility of massive intra operative hemorrhage; In these patients, the most common orthognatic surgery is only shaving of expansive lesions in maxilla or segmental osteotomies. In this paper, we report a thalassemic patient in which maxillary impaction surgery and chin osteotomy were carried out simultaneously. Case report: Patient was a 20 years old woman with thalassemia major complaining from facial deformity. Her problem consists of maxillary protrusion, severe gummy smile, increased lower facial height and deficient chin. After complete Hematologic consideration, simultaneous maxillary impaction and advancement genioplasty was accomplished. Six months follow up showed stable results.