گزارش مورد: گزارش اداره بيهوشي يك مورد متيل مالونيل اسيدمي

nesthetic Management of a Case of Methyl Malonyl Acidemia

Methylmalonyl - coenzyme A deficiency is an inborn error of metabolism that ean result in the formation of methylmalonic acidemia. Experience with anesthesia is limited, and recommendations are based more on theory than on clinieal experience. This study demonstrated a 4 years old boy with methylmalonyl acidemia. Then the presentation of this patient we will discussed management of anesthesia.